Tumefactive multiple sclerosis requiring emergency craniotomy: case report and literature review.

نویسندگان

  • Pablo M Munarriz
  • Ana M Castaño-Leon
  • Rafael Martinez-Perez
  • Aurelio Hernandez-Lain
  • Ana Ramos
  • Alfonso Lagares
چکیده

Multiple sclerosis (MS) is a demyelinating disease of the central nervous system, characterized by focal neurological dysfunction with a relapsing and remitting course. Tumor-like presentation of MS (or "tumefactive"/"pseudotumoral" presentation) has been described before with a certain frequency; it consists of a large single plaque (>2cm) with presence of edema and mass effect and it is hard to distinguish from a brain tumor. However, we present a very rare case of a 53-year-old woman with a right temporal mass that turned out to be a MS plaque, who deteriorated within hours (brain herniation with loss of consciousness and unilateral mydriasis) and required an emergency craniotomy. We also present a review of the literature. It appears that only 4 cases of emergency craniotomy/craniectomy required in a patient with a tumor-like MS plaque have been reported before.

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عنوان ژورنال:
  • Neurocirugia

دوره 24 5  شماره 

صفحات  -

تاریخ انتشار 2013